Ormond syndrome (retroperitoneal fibrosis)

General: Periureteral fibrosis that constricts ureter; most frequent in males; average age at onset is 46 years in males and 32 years in females; etiology possibly is a fasciculitis of collagen disease; clinical variant of multiple fibrosclerosis.

Ocular: Exophthalmos; orbital pseudotumor; nongranulomatous panuveitis.

Clinical: Pain in back progressing to ureteral colic or abdominal pain without specific localization; vomiting; nausea; anorexia; malaise; fatigue; weight loss; constipation; diarrhea; pyelonephritis.

Aylward GW et al. Orbital involvement in multifocal fibrosclerosis. Br J Ophthalmol 1995; 79:246-249.

Doi M, Uji Y. A case of uveitis associated with idiopathic retroperitoneal fibrosis. Am J Ophthalmol 1994; 117: 358-362.

Levine MR, et al. Multifocal fibrosclerosis. Report of a case of bi lateral idiopathic sclerosing pseudotumor and retroperitoneal fibrosis. Arch Ophthalmol 1993; 111:841-843.

Magalini SI, Scrascia E. Dictionary of Medical Syndromes, 2nd ed. Philadelphia: JB Lippincott, 1981.

Ormond JK. Bilateral ureteral obstruction due to envelopment and compression by an inflammatory retroperitoneal process. J Urol 1935; 59:1072-l079.