Behçet syndrome (dermato-stomato-ophthalmic syndrome; oculobuccogenital syndrome; gilbert syndrome) 133

General: Virus infection?; occurs in adults; chronic disease; complete remission is rare; etiology is unknown.

Ocular: Muscle palsies (occasional); nystagmus (occasional); conjunctivitis; hypopyon; iritis; recurrent uveitis; keratoconjunctivitis sicca; keratitis; vitreous hemorrhages; thrombophlebitis retinal veins (occasional); retinal hemorrhages; optic neuritis (occasional); macular edema; optic nerve atrophy; retinitis; secondary glaucoma; retinal vasculitis; disk edema; panophthalmitis; optic neuropathy; skin lesions, posterior uveitis and systemic complications have been associated with loss of vision with this disorder; corneal immune ring opacity.

Clinical: Aphthous lesions of mucous membranes of the mouth and genitalia; cerebellar signs; convulsions; paraplegia; skin erythema (multiforme, bullosum); arthritis; urethritis; glossitis; recurrent fever.

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